Klippel-Trenaunay Syndrome (KTS) Print E-mail

What is it?

Klippel-Trenaunay Syndrome is a rare congenital vascular disorder with no known cause. Klippel-Trenaunay (KTS) may include the following:Birthmark Ireland

a) Port-wine Stain.
b) Excessive growth of the soft tissue/bones.
c) Venous malformations and lymphatic abnormalities.

Complications can include: bleeding, cellulitis, venous thrombosis or pulmonary embolism. KTS is usually limited to one limb, but may occur in multiple limbs and/or head or trunk area. Each case is unique and there is no known cure. Research is on-going.

Birthmark IrelandMRI scans are useful in determining the scope of the syndrome and how best to manage it.

Conservative treatment is usually effective. Elastic garments often relieve the effects of lymphoedema, and protect the limbs from trauma, decreasing the chances of bleeding. Laser therapy can reduce the port wine stains.

Further information.

Further information can be obtained from the following website:

Birthmark Ireland